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대한생식의학회지 제30권 제2호 2010년
자궁내막증이 동반된 Mayer-Rokitansky-Küster-Hauser 증후군의 수술적 치료경험 1례
울산대학교 의과대학 서울아산병원 산부인과학교실
박정열, 김정훈,강천식,이지영,박소연,김성훈,채희동,강병문
A Case of Mayer-Rokitansky-Küster-Hauser Syndrome Accompanying Endometriosis
Jeong Yeol Park
Department of Obstetrics and Gynecology, College of Medicine, University of Ulsan, Asan Medical Center, Seoul, Korea
The Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome refers to a condition which presents as normal female secondary sex characteristics, normal external genitalia, congenital absence of the internal vagina, usually a rudimentary uterus in the form of bilateral noncanaliculated muscular buds, and normal tubes and ovaries with normal cytogenetic and endocrine evaluation, frequent association of renal, skeletal and other congenital anomalies. However, rarely, whole uterus or a segment of uterus may be present, but lacking a conduit to the introitus. If a partial endometial cavity is present in a segment of uterus, cyclic abdominal pain may be a complaint and furthermore endometiosis can be developed. Recently, we experienced a case of MRKH syndrome with the segments of uterus accompanying endometriosis in young woman. We present this case with a brief review of literatures.
키워드 : MRKH Syndrome, Endometriosis
교신저자 : chnkim@amc.seoul.kr
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